Von Hippel Lindau Syndrome with Renal Cell Carcinoma, Pancreas Serous Cystadenoma, Hemangioblastoma and NET Demonstrated on Ga-68 DOTATATE PET-CT and FDG PET-CT Imaging

Abstract

Von Hippel–Lindau disease (VHL), also known as Von Hippel–Lindau syndrome, is a rare genetic disorder with multisystem involvement (1).  Imaging plays an important role in the evaluation of cancer patients. In recent years, much attention has been focused on 68Ga-PSMA PET-CT. We hereby, report the rare case of a Von Hippel Lindau Syndrome with renal cell carcinoma, pancreas cystadenoma, hemangioblastoma and pancreatic NET demonstrated on both Ga-68 PSMA and FDG PET-CT imaging.